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| Imaging diagnosis of Peutz-Jeghers Syndrome: a report of two cases with literature reviews |
| MA Aidong1, SHI Dongmei2, ZHANG Qianli3 |
1. Department of Radiology, Jining NO.1 People's Hospital, Jining 272001 China;
2. Department of Dermatology, Jining NO.1 People's Hospital;
3. Radiology department, Guizhou cancer hospital |
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Abstract Objective This study aimed to improve the diagnosis and management of PJS.Methods The clinical data and imaging findings of two PJS cases were retrospectively analyzed.Results Both cases were clinically diagnosed as Peutz-Jeghers syndrome with a history of abdominal pain, secondary intussusception of the small intestine polyps and intestinal obstruction, and one of the cases complicated with breast cancer and uterus diseases. The imaging findings consistent with the clinical manifestations.Conclusion Patients with PJS usually present hematochezia, abdominal pain, bowel obstruction. They also have an increasing risk of developing cancer or transformation to malignant polyps in the gastrointestinal tract and other organs. Imaging finding and clinical features of PJS have certain characteristics. Surgical resection may appropriately be used for the patients with polyps.
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Received: 08 June 2018
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